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Conditions of optimal GLB1 Enzyme performance should be determined experimentally by the investigator.
Price/availability/specifications subject to change without notice. Unless otherwise indicated, our catalog and customized products are for research use only and not intended for human or animal diagnostic or therapeutic use.
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Introduction
Beta Galactosidase is a lysosomal Beta Galactosidase that hydrolyzes the terminal Beta Galactose from Ganglioside and Keratan sulfate. In lysosome, the mature Beta Galactosidase protein associates with Cathepsin A and Neuraminidase 1 to form the lysosomal multienzyme complex . An alternative splicing at the RNA level of Beta Galactosidase results a catalytically inactive Beta Galactosidase that plays an important role in vascular development. Defects of Beta-galactosidase (GLB1) are the cause of diseases like GM1-gangliosidosis which is a lysosomal storage disease and Morquio Syndrome B that cause patients to have abnormal elastic fibers. More than 100 mutations have been identified for Beta Galactosidase, which result in different residual activities of the mutant enzymes and a spectrum of symptoms in the two related diseases.
BP000705-ENZ-041: Recombinant E.coli Beta-galactosidase (GLB1) Enzyme
Source: E. coli-derived.
Predicted molecular mass: 114 kDa.
Purity: > 95% by SDS-PAGE.
Formulation: Beta-Galactosidase (1 mg/1ml) is formulated in 8 M urea, 20 mM Tris-HCl pH 8.0, and 10mM beta-mercaptoethanol.
Shipping: The product is shipped at ambient temperature. Upon receipt, store it immediately at the temperature recommended below.
Stability & Storage: Use a manual defrost freezer and avoid repeated freeze-thaw cycles.
12 months from date of receipt, -20 to -70°C as supplied.
Other GLB1 Enzymes:
Recombinant Human GLB1 Enzyme
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