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Dysferlin Antibody

Dysferlin, limb girdle muscular dystrophy 2B (autosomal recessive)

Catalog No. Product Name Size List Price (US$) Quantity
PA001501-C0176 Dysferlin Polyclonal Antibody 50 ug 250.00
PA001501-C0176 Dysferlin Polyclonal Antibody 100 ug 350.00
Description

Introduction
Dysferlin also known as dystrophy-associated fer-1-like protein is a protein that in humans is encoded by the DYSF gene. Dysferlin is linked with skeletal muscle repair. A defect in the DYSF gene, located on chromosome 2p12-14, results in either of two types of muscular dystrophy; Miyoshi myopathy (MM) and Limb-girdle muscular dystrophy type 2B (LGMD2B). A reduction or absence of dysferlin usually becomes apparent in the third or fourth decade of life and is characterised by weakness and wasting of various voluntary skeletal muscles.

PA001501-C0176: Dysferlin Polyclonal Antibody

Rabbit Polyclonal Antibody.
Specificity/Sensitivity: Dysferlin antibody detects endogenous levels of total Dysferlin protein.
Applications: WB: 1:300~1:1000 ELISA: 1:10000.
Reactivity: Human, Mouse.
Immunogen: The antiserum was produced against synthesized peptide derived from human Dysferlin.
Purification: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Form of Antibody: Rabbit IgG in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150 mM NaCl, 0.02% sodium azide and 50% glycerol.

Storage/Stability: Stable for 1 year at -20°C and 3 months at 4°C. For maximum recovery of the product, centrifuge the original vial after thawing and before removing the cap. Aliquot to avoid repeated freezing and thawing.

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